Journal of Clinical Oncology MAY 31, 2024

Lorlatinib Versus Crizotinib in Patients With Advanced ALK-Positive Non–Small Cell Lung Cancer: 5-Year Outcomes From the Phase III CROWN Study

Benjamin J. Solomon, Todd M. Bauer, Tony S. K. Mok, et al.

Bottom Line

In patients with previously untreated, advanced ALK-positive non–small cell lung cancer, first-line lorlatinib demonstrated unprecedented long-term efficacy with a 5-year progression-free survival rate of 60% compared to 8% with crizotinib.

Key Findings

1. At a median follow-up of 60.2 months, the median progression-free survival (PFS) was not reached in the lorlatinib group, compared to 9.1 months in the crizotinib group (hazard ratio [HR], 0.19; 95% CI, 0.13 to 0.27).
2. The 5-year PFS rate was 60% with lorlatinib versus 8% with crizotinib.
3. Lorlatinib significantly delayed intracranial progression, with a 94% reduction in the risk of intracranial progression compared to crizotinib (HR, 0.06; 95% CI, 0.03 to 0.12).
4. Treatment-emergent grade 3 or 4 adverse events were more frequent with lorlatinib (77%) than with crizotinib (57%), primarily driven by metabolic effects such as hypertriglyceridemia, hypercholesterolemia, and weight gain.
5. CNS-related adverse events occurred in 42% of patients treated with lorlatinib, with 86% being grade 1 or 2, demonstrating a manageable neurocognitive safety profile.

Study Design

Design
RCT
Open-Label
Sample
296
Patients
Duration
60.2 mo
Median
Setting
Multicenter, international
Population Patients with previously untreated, stage IIIB or IV ALK-positive non–small cell lung cancer.
Intervention Lorlatinib 100 mg orally once daily.
Comparator Crizotinib 250 mg orally twice daily.
Outcome Progression-free survival (PFS) by blinded independent central review.

Study Limitations

The study was open-label, which could introduce bias in investigator-assessed outcomes, though the primary analysis utilized blinded independent central review in earlier stages.
The frequency of grade 3–4 adverse events associated with lorlatinib necessitates rigorous long-term management of metabolic and neurocognitive side effects.
Overall survival data remain immature, preventing a definitive conclusion on the mortality benefit at this time.
The findings are specific to ALK-positive NSCLC and may not be generalizable to other driver-mutation populations.

Clinical Significance

The CROWN trial results establish lorlatinib as the preferred first-line standard of care for advanced ALK-positive NSCLC. The unprecedented 5-year PFS and robust CNS activity provide a new benchmark for targeted therapy efficacy, significantly altering the treatment paradigm by providing durable disease control that potentially avoids the need for early sequential TKI therapy.

Historical Context

Crizotinib was the first-generation ALK-TKI that initially established the efficacy of targeting ALK rearrangements in NSCLC. Subsequent generations, including alectinib and brigatinib, improved upon crizotinib's efficacy and brain penetration. The CROWN trial represents the culmination of this evolution, demonstrating that the third-generation inhibitor, lorlatinib, provides superior, long-term systemic and intracranial control, setting a new high-water mark for molecularly targeted therapy.

Guided Discussion

High-yield insights from every perspective

Med Student
Medical Student

What is the primary mechanism of action of lorlatinib, and why is its ability to penetrate the blood-brain barrier (BBB) clinically significant for patients with ALK-positive non-small cell lung cancer (NSCLC)?

Key Response

Lorlatinib is a third-generation ALK tyrosine kinase inhibitor (TKI). Unlike first-generation crizotinib, it was macrocyclized to enhance potency and BBB penetration. This is crucial because the central nervous system (CNS) is a common site of relapse and metastasis in ALK-positive NSCLC; effectively treating or preventing brain metastases is a key component of improving long-term survival.

Resident
Resident

In the context of the 5-year CROWN study results, how should a clinician manage the specific metabolic and neurocognitive side effects unique to lorlatinib compared to earlier-generation ALK inhibitors?

Key Response

Lorlatinib is associated with unique toxicities including hyperlipidemia, weight gain, and cognitive effects (e.g., memory impairment or mood changes). Residents must recognize that while lorlatinib has superior efficacy, management requires frequent lipid monitoring (often requiring statins) and proactive screening for neuropsychiatric symptoms, which may necessitate dose interruptions or reductions without necessarily compromising the unprecedented progression-free survival (PFS) benefit.

Fellow
Fellow

The CROWN trial reports a 5-year PFS rate of 60% for lorlatinib versus 8% for crizotinib. How does this result impact the sequence of therapy for a patient who might otherwise have started on a second-generation TKI like alectinib or brigatinib?

Key Response

While alectinib and brigatinib are established first-line options, the CROWN data shows a hazard ratio of 0.19, the lowest ever reported in advanced NSCLC. Fellows must weigh this superior 'front-loading' of the most potent agent against the risk of exhausting treatment options, especially since lorlatinib can overcome many resistance mutations (like G1202R) that develop after second-generation TKIs. The debate centers on whether starting with the 'best' drug (lorlatinib) outweighs the traditional sequential approach.

Attending
Attending

With the 5-year PFS curve for lorlatinib appearing to plateau at 60%, can we now realistically discuss 'functional cure' or exceptional long-term survivorship in the first-line metastatic ALK+ setting?

Key Response

An attending-level perspective recognizes that a 60% PFS at five years is transformative. This suggests a subset of patients may achieve durable, long-term remission previously unseen in metastatic lung cancer. This shift requires re-evaluating patient counseling from a 'palliative' mindset to one of 'chronic disease management' or 'long-term survivorship,' focusing on quality of life and long-term toxicity monitoring.

Scholarly Review

Critical appraisal through the lens of expert reviewers and guideline development

PhD
PhD

From a methodological standpoint, how does the choice of crizotinib as the control arm in the CROWN trial—given that it was already being superseded by second-generation TKIs during the study period—limit our ability to perform a network meta-analysis comparing lorlatinib to alectinib?

Key Response

The use of an active but 'sub-optimal' control (crizotinib) creates a 'trial-lag' effect. While the efficacy against crizotinib is clear, the lack of a head-to-head comparison with alectinib or brigatinib means researchers must rely on cross-trial comparisons and indirect treatment comparisons (ITCs). PhDs would critique the hazard ratios generated via ITCs, noting that differences in patient populations and CNS imaging protocols across trials can confound the perceived superiority of one third-generation agent over second-generation ones.

Journal Editor
Journal Editor

Despite the remarkable PFS benefit, the overall survival (OS) data in the CROWN 5-year update remains immature. What are the editorial concerns regarding the potential for subsequent treatments to confound OS, and is PFS a sufficient primary endpoint for regulatory and clinical consensus in this specific genetic niche?

Key Response

Editors must evaluate if PFS is a valid surrogate for OS in ALK+ disease, where patients often live for many years across multiple lines of therapy. With a 60% PFS at five years, waiting for mature OS data could take a decade. The editorial challenge is to determine if the magnitude of PFS improvement (HR 0.19) is so clinically significant that it justifies practice change even in the absence of a definitive OS advantage, which may be perpetually masked by crossover and subsequent TKI use.

Guideline Committee
Guideline Committee

Based on the 5-year CROWN outcomes, should lorlatinib be elevated to the sole 'Preferred' Category 1 recommendation for ALK+ NSCLC, and how should guidelines address its use in patients with baseline brain metastases vs. those without?

Key Response

Current NCCN and ESMO guidelines include lorlatinib, alectinib, and brigatinib as first-line options. The committee must decide if the 60% 5-year PFS justifies prioritizing lorlatinib over alectinib (which has a 5-year PFS of approx. 35% in the ALEX trial). The rationale must balance the superior intracranial efficacy and PFS of lorlatinib against the more favorable safety profile of second-generation agents, potentially leading to a nuanced recommendation based on CNS disease burden and patient comorbidities.

Clinical Landscape

Noteworthy Related Trials

2014

PROFILE 1014 Trial

n = 343 · NEJM

Tested

Crizotinib

Population

Treatment-naive patients with advanced ALK-positive NSCLC

Comparator

Platinum-doublet chemotherapy

Endpoint

Progression-free survival

Key result: Crizotinib demonstrated significantly longer progression-free survival compared to standard chemotherapy in previously untreated ALK-positive NSCLC.
2017

ALEX Trial

n = 303 · NEJM

Tested

Alectinib

Population

Treatment-naive patients with advanced ALK-positive NSCLC

Comparator

Crizotinib

Endpoint

Progression-free survival

Key result: Alectinib significantly improved progression-free survival and showed reduced central nervous system progression compared to crizotinib.
2018

ALTA-1L Trial

n = 275 · NEJM

Tested

Brigatinib

Population

Treatment-naive patients with advanced ALK-positive NSCLC

Comparator

Crizotinib

Endpoint

Progression-free survival

Key result: Brigatinib showed superior efficacy and a significantly higher rate of progression-free survival compared to crizotinib in the first-line setting.

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