New England Journal of Medicine May 04, 2017

Evolocumab and Clinical Outcomes in Patients with Cardiovascular Disease

Marc S Sabatine, Robert P Giugliano, Anthony C Keech, Narimon Honarpour, Stephen D Wiviott, Sabina A Murphy, Julia F Kuder, Huei Wang, Thomas Liu, Scott M Wasserman, Peter S Sever, Terje R Pedersen; FOURIER Steering Committee and Investigators

Bottom Line

In patients with atherosclerotic cardiovascular disease already on statin therapy, the addition of the PCSK9 inhibitor evolocumab safely reduced LDL cholesterol to a median of 30 mg/dL and significantly decreased the risk of major adverse cardiovascular events.

Key Findings

1. EvolocumabreducedLDLcholesterollevelsby59%fromamedianbaselineof92mg/dLto30mg/dLat48weeks(P<0.001)[1.1].
2. Treatment with evolocumab significantly reduced the incidence of the primary composite endpoint (CV death, MI, stroke, hospitalization for unstable angina, or coronary revascularization), occurring in 9.8% (1,344 patients) of the evolocumab group versus 11.3% (1,563 patients) of the placebo group (HR 0.85; 95% CI, 0.79-0.92; P<0.001).
3. The key secondary composite endpoint (CV death, MI, or stroke) was also significantly reduced, occurring in 5.9% (816 patients) with evolocumab versus 7.4% (1,013 patients) with placebo (HR 0.80; 95% CI, 0.73-0.88; P<0.001).
4. There was no significant difference in cardiovascular mortality (HR 1.05; 95% CI 0.88-1.25) or all-cause mortality between the groups during the trial period.
5. Safety profiles were similar between the groups, with no significant difference in neurocognitive events or new-onset diabetes, though injection-site reactions were slightly more common with evolocumab (2.1% vs. 1.6%).

Study Design

Design
RCT
Double-Blind
Sample
27,564
Patients
Duration
2.2 yr
Median
Setting
Multinational
Population Patients with atherosclerotic cardiovascular disease (history of MI, stroke, or symptomatic peripheral artery disease) and LDL cholesterol levels >=70 mg/dL (or non-HDL >=100 mg/dL) who were receiving optimized statin therapy.
Intervention Evolocumab (140 mg every 2 weeks or 420 mg monthly) administered as subcutaneous injections.
Comparator Matching placebo administered as subcutaneous injections.
Outcome Composite of cardiovascular death, myocardial infarction, stroke, hospitalization for unstable angina, or coronary revascularization.

Study Limitations

The relatively short median follow-up of 2.2 years may have been insufficient to detect a mortality benefit, as survival curves in lipid-lowering trials often require more than 2 years to separate [1.5].
The highly selected population (established ASCVD on statin therapy) means findings may not completely extrapolate to lower-risk, primary prevention populations.
The cost of evolocumab is substantially higher than statins, raising debates over its cost-effectiveness in broad populations.
Subsequent readjudication of deaths by independent researchers (RIAT initiative) sparked controversy regarding potential misclassification of cardiovascular versus non-cardiovascular deaths, though the primary trialists defended the integrity of their blinded adjudication process.

Clinical Significance

The FOURIER trial was a landmark study demonstrating that profound reduction of LDL cholesterol below current guideline targets (to a median of 30 mg/dL) using a PCSK9 inhibitor is safe and yields significant clinical benefit in reducing major cardiovascular events in patients with established ASCVD who are already receiving statin therapy. This cemented the 'lower is better' lipid hypothesis and prompted more aggressive LDL-C targets in subsequent clinical guidelines.

Historical Context

For decades, statins were the foundation of lipid-lowering therapy. While the IMPROVE-IT trial in 2015 demonstrated that non-statin lipid lowering via ezetimibe modestly improved cardiovascular outcomes, the magnitude of LDL-C reduction was small. PCSK9 inhibitors emerged as a revolutionary therapeutic class capable of massive LDL-C reductions, but their effect on hard clinical outcomes was previously unknown. The FOURIER trial was the first major cardiovascular outcomes trial to validate the clinical efficacy and safety of PCSK9 inhibition.

Guided Discussion

High-yield insights from every perspective

Med Student
Medical Student

How does the mechanism of action of evolocumab complement that of statin therapy to produce a synergistic reduction in LDL cholesterol?

Key Response

Statins inhibit HMG-CoA reductase, decreasing intracellular cholesterol synthesis and leading to an upregulation of surface LDL receptors. However, statins also increase the expression of PCSK9, a protein that binds to LDL receptors and promotes their lysosomal degradation instead of recycling. Evolocumab is a monoclonal antibody that binds to PCSK9, preventing this degradation. This allows the LDL receptors upregulated by statins to remain on the hepatocyte surface longer, massively increasing the clearance of LDL cholesterol from the bloodstream.

Resident
Resident

Given the 15 percent relative risk reduction in the primary endpoint seen in the FOURIER trial, how do you determine which ASCVD patients on maximal statin therapy will derive the highest absolute risk reduction from the addition of evolocumab?

Key Response

Absolute risk reduction (ARR) and Number Needed to Treat (NNT) depend heavily on the patient's baseline cardiovascular risk. According to the data, patients with 'very high-risk' features—such as multiple prior myocardial infarctions, recent acute coronary syndrome, multivessel coronary artery disease, or symptomatic peripheral arterial disease—have the highest baseline event rates. Therefore, prescribing evolocumab to these patients yields a much larger absolute benefit and a lower NNT compared to a stable patient with a single distant, uncomplicated event.

Fellow
Fellow

The FOURIER trial achieved a median LDL-C of 30 mg/dL, with a significant proportion of patients dropping below 20 mg/dL or even 10 mg/dL. What are the clinical and theoretical safety implications of maintaining such unprecedentedly low LDL-C levels, particularly concerning neurocognitive function and steroidogenesis?

Key Response

Historically, there was concern that ultra-low LDL-C might impair cell membrane integrity, steroid hormone synthesis, and neurocognitive function, as the brain relies heavily on cholesterol. However, FOURIER and its dedicated EBBINGHAUS neurocognitive substudy demonstrated no increase in cognitive decline, hemorrhagic stroke, or other adverse events at these ultra-low levels. This supports the biological concept that peripheral tissues and the central nervous system can synthesize sufficient cholesterol locally and independently of circulating apolipoprotein B-containing lipoproteins.

Attending
Attending

The FOURIER trial demonstrated a significant reduction in non-fatal cardiovascular events but failed to show a cardiovascular mortality benefit during its 2.2-year median follow-up. How should this discrepancy influence your shared decision-making conversations with patients regarding the high cost and value of long-term PCSK9 inhibitor therapy?

Key Response

When counseling patients, it is essential to frame the trial's short follow-up duration. Lipid-lowering trials typically require 3 to 5 years to show a mortality benefit due to the 'legacy effect' and the time it takes for plaque stabilization to translate into survival gains. While short-term mortality was unaffected, the prevention of non-fatal strokes and MIs has profound implications for a patient's functional independence and quality of life. The conversation must balance this robust reduction in morbidity against the financial toxicity and injection burden of the medication.

Scholarly Review

Critical appraisal through the lens of expert reviewers and guideline development

PhD
PhD

The Kaplan-Meier curves for the primary composite endpoint in the FOURIER trial separate progressively over time. How does the relatively short median follow-up of 2.2 years affect the statistical interpretation of the hazard ratio, specifically regarding the proportional hazards assumption and the time-dependent nature of the treatment effect?

Key Response

The progressive separation of the Kaplan-Meier curves suggests that the relative risk reduction increases with longer duration of treatment, which implies a non-constant hazard ratio over time. This violates the strict proportional hazards assumption of the Cox model, meaning the reported overall hazard ratio is an average that likely underestimates the drug's true long-term efficacy. Researchers must account for this time-dependent treatment effect, acknowledging that short-duration trials in lipid lowering often capture early non-fatal events but are statistically underpowered to detect delayed mortality benefits.

Journal Editor
Journal Editor

During peer review, how critically should the editorial board evaluate the choice of a primary composite endpoint that includes 'softer' physician-driven events like coronary revascularization, compared to the 'hard' secondary composite endpoint of CV death, MI, or stroke?

Key Response

Editors must scrutinize composite endpoints because statistical significance can be disproportionately driven by softer, highly prevalent endpoints like revascularization or hospitalization for unstable angina, which are subject to physician bias and regional practice variations. In FOURIER, the primary endpoint was indeed heavily driven by revascularization and MI, while CV death was unchanged. A rigorous review ensures the manuscript accurately reflects whether the intervention primarily prevents hard ischemic events or merely delays elective procedures, preventing overstatement of the clinical impact.

Guideline Committee
Guideline Committee

How do the results of the FOURIER trial directly inform the 2018 AHA/ACC/AACVPR/AAPA/ABC/ACPM/ADA/AGS/APhA/ASPC/NLA/PCNA Guideline on the Management of Blood Cholesterol regarding the specific LDL-C threshold for adding non-statin therapies in secondary prevention?

Key Response

The FOURIER trial provided pivotal evidence that lowering LDL-C well below previous targets is safe and effective. This directly informed the 2018 AHA/ACC guidelines, which established an LDL-C threshold of 70 mg/dL (1.8 mmol/L). For patients with clinical ASCVD judged to be at 'very high risk,' the guidelines give a Class I recommendation to add ezetimibe, and subsequently a PCSK9 inhibitor like evolocumab (Class IIa), if their LDL-C remains at or above 70 mg/dL despite maximally tolerated statin therapy, formally endorsing an 'even lower is better' strategy for the highest risk tiers.

Clinical Landscape

Noteworthy Related Trials

2004

PROVE IT-TIMI 22

n = 4,162 · NEJM

Tested

Atorvastatin 80mg daily

Population

Patients hospitalized for an acute coronary syndrome in the preceding 10 days

Comparator

Pravastatin 40mg daily

Endpoint

Composite of death from any cause, myocardial infarction, unstable angina requiring rehospitalization, revascularization, or stroke

Key result: Intensive lipid-lowering statin therapy provided significantly greater protection against death or major cardiovascular events than standard therapy.
2015

IMPROVE-IT

n = 18,144 · NEJM

Tested

Ezetimibe 10mg daily plus simvastatin 40mg daily

Population

Patients stabilized after acute coronary syndrome with LDL cholesterol levels between 50 to 125 mg/dL

Comparator

Simvastatin 40mg daily plus placebo

Endpoint

Composite of cardiovascular death, nonfatal myocardial infarction, unstable angina requiring rehospitalization, coronary revascularization, or nonfatal stroke

Key result: Adding ezetimibe to statin therapy resulted in incrementally lower LDL cholesterol levels and correspondingly improved cardiovascular outcomes.
2018

ODYSSEY OUTCOMES

n = 18,924 · NEJM

Tested

Alirocumab 75mg or 150mg subcutaneously every 2 weeks

Population

Patients with acute coronary syndrome in the previous 1 to 12 months

Comparator

Placebo

Endpoint

Composite of coronary heart disease death, nonfatal myocardial infarction, fatal or nonfatal ischemic stroke, or unstable angina requiring hospitalization

Key result: Alirocumab significantly reduced the risk of major adverse cardiovascular events compared to placebo in patients with recent ACS.

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